Prosthodontic rehabilitation of a pediatric patient with hypohidrotic ectodermal dysplasia: a case report
Keywords:Hypohidrotic ectodermal dysplasia, Christ-Siemens-Touraine syndrome, Prosthetic rehabilitation, Multidisciplinary management, Pediatric patient
The aim of this case report was to prosthodontically rehabilitate and boost the psychological development of the patient. Ectodermal dysplasia is a hereditary condition presented with abnormal development of tissues of ectodermal origin such as hair, skin, nails, and teeth. This condition generally presented with following signs and symptoms; dental abnormalities, onychodysplasia, hypohidrosis, and hypotrichosis. Ectodermal dysplasia usually has an X-linked recessive trait, with most common being of hypohidrotic ectodermal dysplasia also known as Christ-Siemens-Touraine syndrome. This case report describes the prosthetic rehabilitation with conventional dentures in maxillary arch and tooth supported overdenture in mandibular arch of a young boy with hypohidrodic ectodermal dysplasia. Prosthetic treatment is very helpful to these patients from functional, psychological, and psychosocial points of view. Need for continued dental treatment is necessary.
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