DOI: http://dx.doi.org/10.18203/issn.2454-2156.IntJSciRep20174090

Prosthetic rehabilitation of a child affected with Albright’s hereditary osteodystrophy: a case report

Ankita Dhareula, Ashima Goyal, Krishan Gauba

Abstract


Albright’s hereditary osteodystrophy is a rare metabolic disease resulting from an inability of the kidneys and bones to respond appropriately to circulating parathyroid hormone (PTH), the principal regulator of calcium and phosphorous levels in the body. The deranged parathyroid hormone levels along with the disturbed metabolism of calcium and phosphorous significantly affects the development and calcification of the dental hard tissues along with the bone matrix. Oral manifestations include multiple impacted and aplastic teeth, tooth hypoplasias, small crowns with blunt roots, thin enamel with large pulp chambers, malocclusion and premature loss of teeth resulting from caries. The present case report highlights the essential dental findings of the child affected with Albright’s osteodystrophy along with highlighting the complete rehabilitation of the case using a combination of maxillary overdenture and mandibular partial prosthesis.


Keywords


Pseudohypoparathyroidism, Hypoplasia, Missing teeth

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References


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