Undifferentiated embryonal sarcoma of liver in a 9-year-old: case report

Zubin A. Mahajan; Sameera R. Mehta; Raman Singh

doi:10.18203/issn.2454-2156.IntJSciRep20204403

Authors

Zubin A. Mahajan Bharati Vidyapeeth University and Medical College, Pune, Maharashtra
Sameera R. Mehta Department of Pathology, Smt. Kashibai Navale Medical College, Pune, Maharashtra
Raman Singh Bharati Vidyapeeth University and Medical College, Pune, Maharashtra

DOI:

https://doi.org/10.18203/issn.2454-2156.IntJSciRep20204403

Keywords:

Embryonal sarcoma, Undifferentiated embryonal sarcoma of the liver, Histopathology

Abstract

The embryonal sarcoma of the liver is an extremely malignant, aggressive and infrequent condition of the liver, predominantly affecting children in the age groups of four to ten. The disease manifests with fever, abdominal pain or mass, nausea and laboratory findings suggestive of liver cell injury. The diagnosis can be made using tumor markers, imaging, immunohistochemistry and histopathology. The multimodal management protocol focuses the use of surgical resection, chemotherapy and radiation to significantly improved survival rates and quality of life in these patients.

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Author Biographies

Zubin A. Mahajan, Bharati Vidyapeeth University and Medical College, Pune, Maharashtra

M.B.B.S., Bharati Vidyapeeth Deemed to be University Medical College, Pune, Maharashtra, India.

Sameera R. Mehta, Department of Pathology, Smt. Kashibai Navale Medical College, Pune, Maharashtra

Junior Resident, Department of Pathology, Smt. Kashibai Navale Medical College, Pune, Maharashtra, India.

Raman Singh, Bharati Vidyapeeth University and Medical College, Pune, Maharashtra

M.B.B.S., Bharati Vidyapeeth Deemed to be University Medical College, Pune, Maharashtra, India.

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