DOI: http://dx.doi.org/10.18203/issn.2454-2156.IntJSciRep20204403

Undifferentiated embryonal sarcoma of liver in a 9-year-old: case report

Zubin A. Mahajan, Sameera R. Mehta, Raman Singh

Abstract


The embryonal sarcoma of the liver is an extremely malignant, aggressive and infrequent condition of the liver, predominantly affecting children in the age groups of four to ten. The disease manifests with fever, abdominal pain or mass, nausea and laboratory findings suggestive of liver cell injury. The diagnosis can be made using tumor markers, imaging, immunohistochemistry and histopathology. The multimodal management protocol focuses the use of surgical resection, chemotherapy and radiation to significantly improved survival rates and quality of life in these patients.


Keywords


Embryonal sarcoma, Undifferentiated embryonal sarcoma of the liver, Histopathology

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References


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